Idiopathic Pulmonary Fibrosis

A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.

Subtype terms (2)

More specific conditions that are subtypes of Idiopathic Pulmonary Fibrosis in the MeSH hierarchy.

Hamman-Rich Syndrome
1 drug experimental
Idiopathic Interstitial Pneumonias
4 drugs (1 approved, 3 experimental)

Drugs by status

Approved for this indication (3)

Phase 4 trials (2)

Phase 3 trials (27)

Phase 2 trials (96)

Phase 1 trials (50)

Other trials (7)

Organizations

Organization Involved with Phase 4 Indications (8)

Organization Involved with Phase 3 Indications (41)

Organization Involved with Phase 2 Indications (88)

Organization Involved with Phase 1 Indications (31)

Organization Involved with Other Experimental Indications (15)

ICD-10 crosswalk

J84.112 — Idiopathic pulmonary fibrosis