Chapter 17 - Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)»Other congenital malformations (Q80-Q89)»Incontinentia pigmenti (Q82.3)
Q82.3
Incontinentia pigmenti
Related indications (MeSH) (2)
A genodermatosis occurring mostly in females and characterized by skin changes in three phases - vesiculobullous, verrucous papillomatous, and macular melanodermic. Hyperpigmentation is bizarre and irregular. Sixty percent of patients have abnormalities of eyes, teeth, central nervous system, and skin appendages.
Pigmentation Disorders8 drugs (7 approved, 1 experimental)
Diseases affecting PIGMENTATION, including SKIN PIGMENTATION.