Chapter 17 - Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)»Congenital malformations of the circulatory system (Q20-Q28)»Pulmonary valve atresia (Q22.0)
Q22.0
Pulmonary valve atresia
Related indications (MeSH) (1)
Pulmonary Atresia2 drugs (1 approved, 1 experimental)
A congenital heart defect characterized by the narrowing or complete absence of the opening between the RIGHT VENTRICLE and the PULMONARY ARTERY. Lacking a normal PULMONARY VALVE, unoxygenated blood in the right ventricle can not be effectively pumped into the lung for oxygenation. Clinical features include rapid breathing, CYANOSIS, right ventricle atrophy, and abnormal heart sounds (HEART MURMURS).